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The Kaleidoscope of the Operative Solutions for Hearing Restoration in Charge Syndrome: A Critical Review

Daniele Marchioni,Marco Carner*,Davide Soloperto,Andrea Sacchetto,Elisabetta Genovese,Livio Presutti

Exclusively full texts, cited in PUBMED and MEDLINE search engines, that contain all the selected keywords “Charge syndrome”, “cochlear implant”, “cochlear implantation”, “bionic ear” and “ear malformation” have been selected to review the literature on surgical bionic hearing restoration in CHARGE syndrome. A total of 20 publications that specifically deal with the topic have been published between January 1999 and February 2017. At least ten main different otologic and oto-neurosurgical approaches have been suggested in bionic fitting. The otologic approaches were aided by a microscope or an endoscope or by a combined technique, with or without mastoidectomy. The review is conclude by proposing a strategy for the surgical bionic treatment of hearing in children with CHARGE syndrome.